3-hydroxyacyl-coenzyme A dehydrogenase deficiency - определение. Что такое 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
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Что (кто) такое 3-hydroxyacyl-coenzyme A dehydrogenase deficiency - определение


Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency         
MEDICAL CONDITION
LCHAD deficiency; Long-chain hydroxyacyl-CoA dehydrogenase deficiency; Long-chain-3-hydroxyacyl-CoA dehydrogenase; Acyl-coa dehydrogenase, long-chain; Long chain acyl CoA; LCHADD; Long-chain acyl-CoA dehydrogenase deficiency; Long-chain-3-hydroxyacyl-coa dehydrogenase
Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare autosomal recessive fatty acid oxidation disorder that prevents the body from converting certain fats into energy. This can become life-threatening, particularly during periods of fasting.
3-hydroxyacyl-coenzyme A dehydrogenase deficiency         
3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare condition that prevents the body from converting certain fats to energy, particularly during fasting. Normally, through a process called fatty acid oxidation, several enzymes work in a step-wise fashion to metabolize fats and convert them to energy.
3-hydroxyacyl-CoA dehydrogenase         
ENZYME
L-3-hydroxyacyl CoA dehydrogenase; 3-Hydroxyacyl CoA dehydrogenase; 3-hydroxyacyl-coenzyme A dehydrogenase; EC 1.1.1.35; (S)-3-hydroxyacyl-CoA:NAD+ oxidoreductase
In enzymology, a 3-hydroxyacyl-CoA dehydrogenase () is an enzyme that catalyzes the chemical reaction

Википедия

3-hydroxyacyl-coenzyme A dehydrogenase deficiency
3-hydroxyacyl-coenzyme A dehydrogenase deficiency is a rare condition that prevents the body from converting certain fats to energy, particularly during fasting. Normally, through a process called fatty acid oxidation, several enzymes work in a step-wise fashion to metabolize fats and convert them to energy.